Medulloblastoma (MB) are malignant embryonic neuroepithelial tumors of the cerebellum, accounting for 25% of primary tumors of the Central Nervous System of childhood, which predominantly grow in the cerebellar vermis and hardly in the cerebellopontine angle (CPA). The study aims to report the surgical management of a childhood medulloblastoma in CPA. The author report the case of a 1-year-old male child who initially presented with right hemifacial weakness for 40 days. Magnetic resonance imaging (MRI) of the skull showed lesion in the cerebellar cistern. Subjected to surgical excision of the lesion with histopathological and immunohistochemical results of medulloblastoma. This neuroectodermal tumor localization is rare and agressive, been an unusual differential diagnosis of lymphomas, schwannoma and meningioma. Thus, histopathology is the most reliable method for diagnosing the tumor.

Keywords: Medulloblastoma, cerebellopontine angle, tumor.